Table 1 Summary of cases of extragenital Müllerian adenosarcoma until 2003 and our case, modified from Murugasu[21]
From: Extragenital Müllerian adenosarcoma with pouch of Douglas location
Authors | Age | Location | Treatment | Follow-up |
|---|---|---|---|---|
Douglas et al. | 18 | Retroperitoneum | Chemotherapy | Died after 10 wks with distant metastases |
Bard et al. | 46 | Pelvic peritoneum | Surgery, chemotherapy | Died after 11 wks with distant metastases |
Clement et al. | 45 | Pelvic peritoneum | Surgery, radiation therapy | Pelvic recurrences; died after 9 mths |
Clement et al. | 73 | Pelvic peritoneum | Surgery | Died after 2 mths |
Clement et al. | 58 | Pelvic peritoneum | Surgery | Local recurrence at 15 mths; lung metastases at 45 mths |
Kao & Norris | 42 | Round ligament | Partial surgery, chemotherapy, radiation therapy | Died of disease after 10 mths |
Russell et al. | 29 | Broad ligament | Surgery, radiation therapy | Local recurrence at 5 mths; symptom free; died of melanoma after 9 yrs |
Vara et al. | 62 | Bladder | Surgery | Disease free at 1 yr |
Roman et al. | 63 | Retroperitoneum | Surgery, chemotherapy, radiation therapy | Multiple recurrences; heart and liver metastases; died of disease after 10 yrs |
Kerner et al. | 32 | Broad ligament | Surgery | Pelvic recurrences at 22 mths |
De Jonge et al. | 16 | Pelvic peritoneum | Surgery, chemotherapy | Disease free at 57 mths |
Kato et al. | 20 | Peritoneum | Surgery | Disease free at 1 yr |
Visvalinga et al. | 50 | Pelvic peritoneum | Surgery, chemotherapy | Died of disease after1 yr |
Ostor et al. | 49 | Pouch of Douglas | Surgery, chemotherapy, radiation therapy | Alive with disease at 18 mths |
Morugasu et al. | 23 | Pouch of Douglas | Surgery, chemotherapy, radiation therapy | Disease free at 1 yr |
Present case | 49 | Pouch of Douglas | - First step: partial surgery; - Second step (after 24 mths): radical surgery and radiation therapy | Local multiple recurrences (after 18 and 24 mths), today disease free |