Characteristics | n | % |
---|---|---|
Age, median (range) | 28 year (16–82 year) | |
 <28yr | 20 | 47.6 |
 ≥28yr | 22 | 52.4 |
Gender | Â | Â |
 Male | 23 | 54.8 |
 Female | 19 | 45.2 |
Histology | Â | Â |
 Embryonal | 16 | 38.1 |
 Alveolar | 21 | 50.0 |
 Pleomorphic | 3 | 7.1 |
 NOS | 2 | 4.8 |
Primary site | Â | Â |
 Orbital | 1 | 2.4 |
 Parameningeal | 26 | 61.9 |
 Non-orbital/non-parameningeal | 15 | 35.7 |
Primary tumor size | Â | Â |
 ≤ 5 cm | 19 | 45.2 |
 > 5 cm | 23 | 54.8 |
Nodal status | Â | Â |
 N0 | 23 | 54.8 |
 N1 | 19 | 45.2 |
Disease status | Â | Â |
 Localized (N0M0) | 21 | 50.0 |
 Regional (N1M0) | 16 | 38.1 |
 Distant (M1) | 5 | 11.9 |
IRS pretreatment staging | Â | Â |
 Stage I | 15 | 35.7 |
 Stage II | 2 | 4.8 |
 Stage III | 20 | 47.6 |
 Stage IV | 5 | 11.9 |
IRS postsurgical grouping | Â | Â |
 Group I | 9 | 21.4 |
 Group II | 11 | 26.2 |
 Group III | 17 | 40.5 |
 Group IV | 5 | 11.9 |
Surgery margins | Â | Â |
 Negative (R0) | 10 | 40.0 |
 Positive (R1/2) | 15 | 60.0 |
Treatment patterns | Â | Â |
 Surgery + Chemotherapy + RT | 23 | 54.7 |
 Surgery + RT | 2 | 4.8 |
 Chemotherapy + RT | 16 | 38.1 |
 RT | 1 | 2.4 |